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Alternating Hemiplegia Of Childhood

Alternating hemiplegia of childhood is a neurological condition characterized by recurrent episodes of temporary paralysis, often affecting one side of the body (hemiplegia)

Prevalence

1-2/100,000

3,310-6,620

US Estimated

5,135-10,270

Europe Estimated

Age of Onset

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ICD-10

G98

Inheritance

Autosomal dominant

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Autosomal recessive

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Mitochondrial/Multigenic

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X-linked dominant

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X-linked recessive

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5 Facts you should know

FACT

1

The most prominent symptom is repeated episodes of weakness or paralysis affecting one side of the body at a time in an alternating fashion

FACT

2

The first symptoms usually begin before the age of 18 months

FACT

3

The severity of AHC and the specific types of episodes that occur can vary dramatically from one individual to another

FACT

4

The length of attacks may also vary from minutes to weeks

FACT

5

All of the known symptoms dissipate immediately upon sleeping

Alternating Hemiplegia Of Childhood is also known as...

Alternating Hemiplegia Of Childhood

Alternating hemiplegia syndrome; AHC; Alternating hemiplegia

What’s your Rare IQ?

Which of the following is a unique characteristic of the alternating hemiplegia of childhood?

Common signs & symptoms

Bilateral tonic-clonic seizure

Grand mal seizures

Autosomal dominant inheritance

Choreoathetosis

Dystonia

Episodic hemiplegia

Episodic quadriplegia

Intellectual disability

Mental deficiency

Nystagmus

Involuntary, rapid, rhythmic eye movements

Top Clinical Trials

At the time this analysis was conducted, there were no treatments in development for this disease.

Top Treatments in Research

At the time this analysis was conducted, there were no treatments in development for this disease.